Literature

Symptoms that Occur in People with Rasmussen Syndrome


“It is important to be aware of the symptoms of Rasmussen syndrome. In addition to seizures, this syndrome can cause paralysis on one side of the body.”

Symptoms that Occur in People with Rasmussen Syndrome

Halodoc, Jakarta – Symptoms of Rasmussen syndrome are quite typical, usually starting from seizures. However, this is different from regular seizures. This is because Rasmussen syndrome is a rare chronic inflammatory neurological disease that usually affects only one hemisphere of the brain.

This condition is a form of inflammation that causes nerve cells to malfunction. This includes autoimmune conditions in which the body’s antibodies can damage one or more organs in the body. In this case, the antibodies attack the brain.

Want to know what the symptoms of this syndrome are and how to treat them? Let’s see more!

Symptoms of Rasmussen’s Syndrome

Symptoms of this syndrome usually appear between the ages of 1 and 14. Seizures are often the first symptom to appear. Apart from seizures, other symptoms that can appear are:

  • Loss of motor and speech skills.
  • Paralysis on one side of the body (hemiparesis).
  • Inflammation of the brain (encephalitis).
  • Mental decline.

This syndrome can cause inflammation that triggers damage to nerve cells, and this causes seizures. Seizures may be very rare at first. However, after a few weeks or months, it becomes very frequent. These symptoms can also occur many times a day.

The seizures that occur are usually focal (partial) and may cause one side of the face or limb to twitch rhythmically. This can happen continuously, it can last for hours or even days. This condition is called epilepsy partialis continua.

Seizure symptoms due to Rasmussen’s syndrome are usually very difficult and sometimes impossible to control with epilepsy drugs. After some time, there will be symptoms of weakness on one side of the body affected by the seizure. As the seizure progresses, this weakness may worsen and lead to loss of function in the arms, legs, or both.

What caused it?

The exact cause of the symptoms of Rasmussen’s syndrome is not clear. However, there is suspicion that this syndrome is an autoimmune disorder. This is a disorder in which the body’s natural defenses (antibodies and T cells) fight its own tissue, mistaking it for a foreign organism for no apparent reason.

Because it is classified as very rare, there is not much information about this syndrome. However, age may be a risk factor, as this syndrome most often occurs in children under the age of 10, although it can affect adolescents and adults as well.

Available Treatment Options

Treatment for the symptoms of Rasmussen syndrome is mostly symptomatic and supportive. Doctors usually prescribe anti-seizure drugs (anticonvulsants) to relieve seizures. Even so, however, in most cases, anticonvulsant drugs are not effective.

Medical treatments targeted at possible autoimmune diseases may be tried, including steroids, immunoglobulins, and tacrolimus. In addition, doctors can also provide immunological therapy, to slow neurological and structural damage. However, these therapies usually do not improve epilepsy or progressive brain atrophy.

In some cases, an operation called cerebral hemisphereectomy may be an option. This may be the only way to treat the seizure symptoms of Rasmussen syndrome and stop neurodevelopmental regression.

However, the difficulty is often deciding the best operating time. This depends on the severity of the seizures and the degree of effect on disease learning and progression.

That is a discussion of the symptoms of Rasmussen syndrome, its causes, and treatment. If you or someone close to you experiences symptoms of this disease, immediately consult a doctor.

If the doctor prescribes medicine, downloads Halodoc just to check your medical needs easily.

Halodoc application download banner
Reference:
Epilepsy Act. Retrieved 2022. Rasmussen Syndrome.
Johns Hopkins Medicine. Accessed in 2022. Understanding Rasmussen Syndrome.
National Institute of Neurological Disorder and Stroke. Retrieved 2022. Rasmussen’s Encephalitis.
National Organization for Rare Disorders. Accessed 2022. Rasmussen Encephalitis.



halodoc.com/gejala-yang-terjadi-pada-pengidap-sindrom-rasmussen”>Source link

Dr. Eka

A doctor, wife and mother of three. Spread the world with valid information.

Related Articles

Leave a Reply

Your email address will not be published.

Back to top button